{"id":8398,"date":"2024-07-15T10:55:00","date_gmt":"2024-07-15T10:55:00","guid":{"rendered":"https:\/\/www.drfz.de\/news\/neue-biomarker-fuer-autoimmunen-kongenitalen-herzblock-identifiziert\/"},"modified":"2025-02-14T14:39:07","modified_gmt":"2025-02-14T14:39:07","slug":"neue-biomarker-fuer-autoimmunen-kongenitalen-herzblock-identifiziert","status":"publish","type":"post","link":"https:\/\/www.drfz.de\/en\/neuigkeiten\/neue-biomarker-fuer-autoimmunen-kongenitalen-herzblock-identifiziert\/","title":{"rendered":"New biomarkers for autoimmune congenital heart block identified"},"content":{"rendered":"\n<section class=\"wp-block-group\">\n<p class=\"wp-block-paragraph\">Ana-Luisa Stefanski and colleagues from the group of Thomas D\u00f6rner, DRFZ and Charit\u00e9 \u2013 Universit\u00e4tsmedizin Berlin, in cooperation with the Department of Obstetrics at Charit\u00e9, have identified new biomarkers and potential causes of autoimmune congenital heart block (CHB). In CHB, the heartbeat of the unborn child significantly slows down, which can result in death of the foetus. This complication occurs in expectant mothers with anti-SSA antibodies, which can occur in Sj\u00f6gren\u2019s disease, systemic lupus erythematosus, but also in some pregnant women without any symptoms. The results have now been published in the journal&nbsp;<em>Annals of the Rheumatic Diseases<\/em>.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">The causes of this rare complication have not been sufficiently investigated, which limits therapeutic interventions. However, it is known that anti-SSA antibodies from the mother enter the foetus via the placenta. These antibodies are directed against protein molecules of cell nuclei and can also attack the heart cells of the foetus.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Approximately 2-3% of babies born to anti-SSA-positive mothers develop CHB. Biomarkers are needed to better identify CHB risk pregnancies. Stefanski et al. found that anti-SSA-positive mothers of CHB-affected children had significantly higher circulating levels of the soluble molecules sPD-L1, sCD86 and s4-1BB in their blood during pregnancy compared to anti-SSA-A-positive pregnant women without complications and healthy pregnant women. In addition, high-risk pregnancies with an increased type I interferon signature could be distinguished from CHB by high sPD-L1 and sCD86 levels.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">The molecule PD-L1 is usually expressed on the trophoblast cells, specific cells of the placenta, and plays a role in the development of immunological tolerance during pregnancy. PD-L1 is important to prevent the foetus from being rejected by the mother\u2019s immune system. Trophoblast cells from CHB placentas have less PD-L1 on the cell surface than healthy placentas. The researchers are now investigating what this means and to what extent therapeutic intervention in this dysregulation offers possibilities for protection against CHB.<\/p>\n<\/section>\n\n\n\n  <section     class=\"section grid-heads alignwide\">\n    <div class=\"container container--center\">\n      \n              <div class=\"grid-heads__items grid grid--4\">\n          \n<article\n  id=\"post-4019\" class=\"teaser-head launimation slideBottom  post-4019 head type-head status-publish has-post-thumbnail hentry department-pa-4-translational-rheumatology liaison-charite-rheumatology-and-clinical-immunology programme-area-tax-programme-area-4 working-group-function-group-leader working-group-tax-b-cell-memory\">\n  <div class=\"teaser-head__image\">\n          <img decoding=\"async\" loading=\"lazy\" sizes=\"auto, 520px\" src=\"https:\/\/www.drfz.de\/wp-content\/uploads\/2024\/12\/Doerner_Thomas-150x100.jpg\" data-src=\"https:\/\/www.drfz.de\/wp-content\/uploads\/2024\/12\/Doerner_Thomas-1024x681.jpg\" data-srcset=\"https:\/\/www.drfz.de\/wp-content\/uploads\/2024\/12\/Doerner_Thomas-1920x1278.jpg 1920w, https:\/\/www.drfz.de\/wp-content\/uploads\/2024\/12\/Doerner_Thomas-1600x1065.jpg 1600w, https:\/\/www.drfz.de\/wp-content\/uploads\/2024\/12\/Doerner_Thomas-1366x909.jpg 1366w, https:\/\/www.drfz.de\/wp-content\/uploads\/2024\/12\/Doerner_Thomas-1024x681.jpg 1024w, https:\/\/www.drfz.de\/wp-content\/uploads\/2024\/12\/Doerner_Thomas-768x511.jpg 768w, https:\/\/www.drfz.de\/wp-content\/uploads\/2024\/12\/Doerner_Thomas-550x366.jpg 550w\" class=\"image image--landscape\" alt=\"\"  width=\"1024\"  height=\"681\">      <\/div>\n  <div class=\"teaser-head__header\">\n    <!--    -->    <!--      -->    <!--    -->    <h2 class=\"h6 teaser-head__title launimation slideBottom\">Prof. Dr. med. Thomas D\u00f6rner<\/h2>\n          <div class=\"teaser-head__role\">\n                          <p class=\"text-label programme_area_function programme_area department\">\n            Programme Area 4, PA 4 \u2013 Translational Rheumatology          <\/p>\n                          <p class=\"text-label working_group_function working_group\">\n            Group leader: B Cell Memory          <\/p>\n                          <p\n            class=\"text-label liaison\">Liaison working group with Charit\u00e9 &#8211; Rheumatology and Clinical Immunology<\/p>\n              <\/div>\n      <\/div>\n\n      <div class=\"teaser-head__contact\">\n              <p class=\"text-label\"><a href=\"mailto:thomas.doerner@charite.de\"\">thomas.doerner@charite.de<\/a><\/p>\n          <\/div>\n    <a href=\"https:\/\/www.drfz.de\/en\/koepfe\/thomas-dorner\/\"\n    aria-describedby=\"post-4019\"\n    title=\"Gehe zum Beitrag\" rel=\"bookmark\"\n    class=\"teaser-head__link button button--small button--arrow button--arrow-link\"><span\n      class=\"visually-hidden\">Prof. Dr. med. Thomas D\u00f6rner<\/span><\/a>\n<\/article>        <\/div>\n          <\/div>\n  <\/section>\n\n\n\n  <section id=\"block_0aa1a90592c763d13f7bf003134c8a7d\" class=\"section links-list  alignwide \">\n    <div class=\"container container--center\">\n      \n      <div class=\"links-list__items-wrap\">\n        \n<div class=\"links-list__items links-list__items--row \">\n      <div class=\"links-list__item  launimation slideBottom\">\n      \n      <a href=\"https:\/\/ard.bmj.com\/content\/annrheumdis\/early\/2024\/07\/12\/ard-2024-226176.full.pdf?ijkey=YtxVw8JBQEEjBTA&#038;keytype=ref\" target=\"_blank\" class=\"h6 links-list__item-title\">original publication<\/a>\n\n              <span class=\"links-list__item-underline\">Stefanski A, Rincon-Arevalo H, Dressler-Steinbach I, et alDysregulation of immune checkpoint molecules as a characteristic of autoimmune congenital heart blockAnnals of the Rheumatic Diseases Published Online First: 12 July 2024. doi: 10.1136\/ard-2024-226176<\/span>\n      \n      <a href=\"https:\/\/ard.bmj.com\/content\/annrheumdis\/early\/2024\/07\/12\/ard-2024-226176.full.pdf?ijkey=YtxVw8JBQEEjBTA&#038;keytype=ref\" target=\"_blank\" class=\"links-list__item-link\">\n        <span class=\"button button--arrow button--arrow-nw button--arrow-link\" ><\/span>\n      <\/a>\n    <\/div>\n  <\/div>\n      <\/div>\n    <\/div>\n  <\/section>\n\n","protected":false},"excerpt":{"rendered":"<p>Lorem ipsum dolor sit amet, consectetur adipiscing elit. Nunc vulputate libero et velit interdum, ac aliquet odio mattis. Class aptent taciti sociosqu ad litora torquent per conubia nostra, per inceptos himenaeos \u2026<\/p>\n","protected":false},"author":1,"featured_media":4735,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[291],"tags":[438,539,497],"programme-area-tax":[182],"working-group-tax":[241],"class_list":["post-8398","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-publications","tag-b-cell-memory","tag-thomas-doerner-en","tag-program-area-4","programme-area-tax-programme-area-4","working-group-tax-b-cell-memory"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>New biomarkers for autoimmune congenital heart block identified - DRFZ<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.drfz.de\/en\/neuigkeiten\/neue-biomarker-fuer-autoimmunen-kongenitalen-herzblock-identifiziert\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"New biomarkers for autoimmune congenital heart block identified - DRFZ\" \/>\n<meta property=\"og:description\" content=\"Lorem ipsum dolor sit amet, consectetur adipiscing elit. 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